TMU’s Department of Pediatric and Preventive Dentistry Treated a Case of Hypohidrotic Ectodermal Dysplasia
The Department of Pediatric & Preventive Dentistry of Teerthanker Mahaveer Dental College and Research Center (TMDC&RC), handled an interesting case of a 5-year-old patient who was presented with Hypohidrotic Ectodermal Dysplasia (HED), a hereditary disorder of ectoderm characterised by a congenital dysplasia of one or more ectodermal structures and their accessory appendages with complete anodontia.
The procedure was guided and supervised by the Head of the Department Dr Ramakrishna Yeluri, Dr Rishika (Reader), Dr Zakiya (Senior Lecturer) and performed by the team of postgraduate students Dr Anubha Jain, Dr Ritu Kumari, Dr Malvika Agarwal and Dr Sushma Singh and Pritam Das Gupta (Intern).
The guardian of this 5-year-old girl came to the department with a major complaint of missing teeth in her upper and lower jaws since birth. Upon clinical and oral examination, it was observed that she had defective hair follicles and eyebrows, frontal bossing with prominent supraorbital ridges, nasal bridge depression and protuberant lips. Intraorally, the child presented with edentulous upper and lower arches and she was having difficulty in eating and speaking.
On radiographic examination, it was observed that all the permanent tooth buds were also missing in the jaws. Hence, the case was diagnosed as Hypohidrotic Ectodermal Dysplasia (HED) with complete anodontia which is a rare hereditary disorder and the condition is thought to occur in 1 of 7 per 100,000 live births.
After the disease was diagnosed the department decided to manage the case by prosthetic rehabilitation of the patient with complete dentures. On her first visit, the patient was motivated for the treatment through behaviour management techniques. Upon the next appointment, primary impressions were made and special trays were fabricated. The secondary impressions were made followed by the fabrication of occlusal rims and jaws.
After that, the fabrication of primary teeth was done with tooth-coloured acrylic and teeth setting was done, the patient was recalled for the try in and the final denture delivery was done. The patient’s guardian was happy and satisfied with the treatment and they expressed their sincere gratitude to the whole team for managing the case as none of the local practitioners was able to handle the case in their locality.
The presentation of this interesting case exemplifies the reach of pediatric dentistry in terms of providing dental treatment and aesthetic rehabilitation for such young patients presenting with hereditary conditions. The Department of Pediatric & Preventive Dentistryalways includes interns to actively participate and allows them to play a supportive role in the team for a better understanding and motivation to choose this speciality as a postgraduate subject.
Teerthanker Mahaveer University's Department of Pediatric & Preventive Dentistry has been performing such explicit cases since 2014, and it is one of its kind in the Moradabad region. Teerthanker Mahaveer Dental College and Research Center (TMDC&RC) is one of the best dental colleges in Delhi NCR and Uttar Pradesh, emphasising practical experience, aided by theoretical knowledge. For more information, please visit, www.tmu.ac.in.
